About Abbott Ketonex-1 Amino Acid-Modified Infant Formula with Iron
Ketonex-1 is a specialized infant formula for maple syrup urine disease (MSUD) or beta-ketothiolase deficiency (BKD). It is free of isoleucine, leucine, and valine, allowing babies with branched-chain amino acid metabolism disorders to consume more intact protein. This formula has a nutrient profile designed especially for infants and toddlers. It helps to supply l-carnitine and taurine in amounts normally found in human milk or animal-based foods, and it includes DHA and ARA to support brain and eye development. Ketonex-1 is non-GMO, lactose-free, and gluten-free.
Key Benefits & Features
- Free of Branched-Chain Amino Acids To Allow Greater Intake of Intact Protein
- Nutrient Profile Designed Specifically for Infants and Toddlers With MSUD and BKD
- Includes DHA and ARA To Promote Cognitive and Visual Development
- Provides L-Carnitine and Taurine in Amounts Normally Found in Breast Milk
- 40% of Energy as Fat for Acceptable Formula Osmolality
- Lactose-Free and Gluten-Free for Babies With Dietary Sensitivities
Abbott Ketonex-1 Amino Acid-Modified Infant Formula with Iron FAQs
What are the instructions for preparation and use?
Use Only As Directed by a Physician
Your baby's health depends on carefully following these directions. Proper hygiene, handling and storage are important when preparing infant formula. Failure to follow these directions could result in severe harm. Ask your baby's doctor if you need to use cooled, boiled water for mixing and if you need to boil (sterilize) bottles, nipples and rings before use.
- Wash your hands, surfaces and utensils
- Pour prescribed amount of water into clean container
- Add prescribed amount of Ketonex-1 powder (and other ingredients if recommended)
- Shake well for 10-15 seconds; if using a blender, mix no more than 5 seconds
- Pour mixture into clean feeding bottles or container; cap
- Once feeding begins, use within 1 hour or discard
What is maple syrup urine disease?
Maple syrup urine disease is a rare, inherited metabolic disorder that affects the body’s ability to metabolize amino acids due to a deficiency in the activity of the branched-chain alpha-ketoacid dehydrogenase complex. It particularly affects the metabolism of amino acids- leucine, isoleucine, and valine.
Ingredients
Powder Unflavored:
Corn Syrup Solids, High Oleic Safflower Oil, Coconut Oil, Soy Oil, L-Alanine, Modified Corn Starch, LProline. Less than 2% of: L-Lysine, L-Arginine, Calcium Phosphate, L-Glutamine, Potassium Phosphate, Glycine, L-Tyrosine, L-Phenylalanine, L-Serine, L-Asparagine, L-Threonine, Sodium Citrate, Potassium Citrate, Magnesium Chloride, L-Histidine, M. Alpina Oil, L-Methionine, Schizochytrium Sp. Oil, Calcium Carbonate, Citric Acid, L-Glutamic Acid, Ascorbic Acid, L-Cystine Dihydrochloride, Inositol, LTryptophan, Choline Chloride, L-Aspartic Acid, L-Carnitine, Taurine, Ferrous Sulfate, Ascorbyl Palmitate, Zinc Sulfate, dl-Alpha-Tocopheryl Acetate, Mixed Tocopherols, Calcium Pantothenate, Niacinamide, Manganese Sulfate, Thiamine Hydrochloride, Copper Sulfate, Vitamin A Palmitate, Riboflavin, Pyridoxine Hydrochloride, Potassium Iodide, Folic Acid, Phylloquinone, Chromium Chloride, Sodium Selenate, Sodium Molybdate, Biotin, Vitamin D3, Vitamin B12, and Salt.
