MSUD Anamix Early Years FAQs

What is Maple Syrup Urine Disease (MSUD) and why does it require a special formula?

Maple Syrup Urine Disease (MSUD) is a rare inherited metabolic disorder in which the body is unable to properly break down three branched-chain amino acids — leucine, isoleucine, and valine. Without treatment, these amino acids accumulate in the blood and can cause serious neurological damage, seizures, and developmental delays. Because standard infant formulas and most foods contain these amino acids, infants with MSUD require a specialized formula that excludes leucine, isoleucine, and valine while still providing all other essential nutrients needed for healthy growth and development.

Why does MSUD Anamix Early Years contain no leucine, isoleucine, or valine?

Leucine, isoleucine, and valine are the branched-chain amino acids that individuals with MSUD cannot metabolize. MSUD Anamix Early Years is specifically designed to exclude these three amino acids while providing a complete profile of all other essential and non-essential amino acids, carbohydrates, fats, vitamins, and minerals. This allows infants with MSUD to meet their protein and nutritional requirements safely, with the precise amounts of branched-chain amino acids they may need provided separately under medical supervision.

What role do DHA and ARA play in this formula?

DHA (docosahexaenoic acid) and ARA (arachidonic acid) are long-chain polyunsaturated fatty acids that support normal infant brain development, eye development, and overall neurological health during the critical first year of life. MSUD Anamix Early Years provides both DHA and ARA to help support healthy development in infants with MSUD who depend on this formula as a primary nutrition source.

What are the prebiotic fibers GOS and FOS and why are they included?

Galacto-oligosaccharides (GOS) and fructooligosaccharides (FOS) are prebiotic fibers that help nourish beneficial bacteria in the infant gut, supporting a healthy digestive environment and contributing to immune system development. MSUD Anamix Early Years contains a GOS/FOS blend providing 0.8g per 100 mL at standard dilution to support digestive health alongside its metabolic nutritional goals.

How is MSUD Anamix Early Years prepared?

To make a standard dilution of 21 kcal per fluid ounce, add 1 unpacked level scoop (5g) of powder to each fluid ounce of cooled, boiled water using only the scoop provided. For accuracy, formula should be weighed on a gram scale. The formula may be mixed with warm or cool boiled water but should never be boiled or microwaved. Always prepare formula with clean hands in a clean environment and use only sterilized bottles and equipment. Follow the preparation schedule provided by your healthcare team.

How should MSUD Anamix Early Years be stored?

Unopened cans should be stored in a cool, dry place away from extreme temperatures. Once opened, use the contents within 2 weeks and replace the lid firmly after each use. Freshly prepared formula is best. If prepared in advance, cool rapidly and refrigerate, using within 24 hours of preparation. Discard any formula remaining in the bottle after 1 hour of feeding has begun.

Who should supervise the use of this formula?

MSUD Anamix Early Years is a specialized medical food that must only be used under medical supervision. It should be prescribed and managed by a healthcare team experienced in metabolic disorders, typically including a metabolic physician and a registered dietitian with expertise in MSUD. It is not suitable as a sole source of nutrition and is only appropriate for infants with a confirmed MSUD diagnosis. Always follow the guidance of your healthcare team for preparation, quantities, and feeding schedules.

Nutrition Facts

Amino Acids, g

Vitamins

Minerals

Ingredients

Corn Syrup Solids, Refined Vegetable Oils (High Oleic Sunflower, Soy, Non-Hydrogenated Coconut, Canola, Sunflower), Galacto-oligosaccharides (GOS) (Milk), L-Lysine L-Glutamate, L-Proline, L-Arginine, Glycine, L-Aspartic Acid, Tricalcium Phosphate, L-Threonine, Citric Acid Esters of Mono- and Diglycerides (CITREM), L-Phenylalanine, L-Serine, L-Histidine, L-Alanine, Potassium Chloride, Fructo-oligosaccharides (FOS), Tripotassium Citrate, L-Cystine, L-Tryptophan, Sodium Phosphate Dibasic, Magnesium Acetate, L-Methionine, M. Alpina Oil*, Choline Bitartrate, C. Cohnii Oil**, L-Glutamine, Sodium Chloride, M-Inositol, L-Ascorbic Acid, L-Glutamic Acid, Taurine, Ferrous Sulfate, Zinc Sulfate, L-Carnitine, DL-Alpha Tocopheryl Acetate, Calcium D-Pantothenate, Niacinamide, Ascorbyl Palmitate, Manganese Sulfate, Cupric Sulfate, Thiamine Hydrochloride, Pyridoxine Hydrochloride, Riboflavin, Vitamin A Acetate, DL-Alpha Tocopherol, Mixed Tocopherols, Potassium Iodide, Chromium Chloride, Folic Acid, Phylloquinone, Sodium Selenite, Sodium Molybdate, D-Biotin, Vitamin D3, Cyanocobalamin.

Contains: Soy Oil, Coconut Oil, Milk.

* A source of Arachidonic Acid (ARA)

** A source of Docosahexaenoic Acid (DHA). Contains GOS/FOS 0.8g per 100 mL.