About Nutricia MSUD Oral Supplement Lophlex LQ Ready-to-Drink Liquid
An isoleucine-, leucine- and valine-free, ready-to-drink medical food containing amino acids, carbohydrates, vitamins, minerals and DHA, based on mixed fruit juices (from concentrate) with natural flavor; for the dietary management of proven maple syrup urine disease (MSUD) in individuals 4 years and older, including pregnant women and women of child-bearing age.
Key Benefits & Features
- Isoleucine-, leucine- and valine-free
- Low volume; low calorie
- Convenient ready-to-drink
- Contains a balanced mixture of other essential and non-essential amino acids, carbohydrates, vitamins, minerals and DHA
- Provides 20g of protein equivalent in one pouch
- 2460 mOsm/kg osmolality
- Does not contain fat thereby allowing greater flexibility in modifying energy intake
Nutricia MSUD Oral Supplement Lophlex LQ Ready-to-Drink Liquid FAQs
What is maple syrup urine disease?
Maple syrup urine disease is a rare, inherited metabolic disorder that affects the body’s ability to metabolize amino acids due to a deficiency in the activity of the branched-chain alpha-ketoacid dehydrogenase complex. It particularly affects the metabolism of amino acids- leucine, isoleucine, and valine.
Nutrition Facts
Serving size: Per Pouch - 4.2 oz
| | Amount per serving |
|---|
| Calories |
120 |
| Protein Equivalent, g |
20 |
| Fat, g |
0.44 |
| DHA, mg |
150 |
| Carbohydrate, g |
9.3 |
| Fiber, g |
0.50 |
Ingredients
Water, Apple Juice Concentrate (34.1%), Grape Juice Concentrate (6.9%), Blackcurrant Juice Concentrate (2.5%), L-Lysine Acetate, L-Proline, Citric Acid, L-Tyrosine, L-Arginine, Glycine, L-Serine, L-Aspartic Acid, L-Alanine, L-Threonine, Corn Syrup Solids, L-Cystine, L-Phenylalanine, Dicalcium Phosphate, L-Histidine, Elderberry Juice Concentrate (0.6%), Maltodextrin, Magnesium Acetate, N-Acetyl L-Methionine, L-Tryptophan, Choline Bitartrate, C. cohnii Oil**, Sugar, Microcrystalline Cellulose, Natural Flavor, Fruit Concentrate, L-Ascorbic Acid, Taurine, Guar Gum, Sun昀氀ower Lecithin, Xanthan Gum, M-Inositol, Potassium Sorbate, Sucralose, Ferrous Lactate, Acesulfame Potassium, Sodium Benzoate, Zinc Sulfate, L-Carnitine, Niacinamide, DL-Alpha Tocopheryl Acetate, Calcium D-Pantothenate, Manganese Sulfate, Cupric Sulfate, Thiamine Hydrochloride, Pyridoxine Hydrochloride, Vitamin A Palmitate, Ribo昀氀avin, Folic Acid, Potassium Iodide, Ascorbyl Palmitate, Mixed Tocopherols, Sodium Molybdate, D-Biotin, Sodium Selenite, Chromium Chloride, Phylloquinone, Vitamin D3, Cyanocobalamin.
**A Source of Docosahexaenoic Acid (DHA).
